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HighQC™ Human IPSC From Foreskin Fibroblast (Skin Fibroblasts Of A Cystinosis Patient)

  • For research use only

Cat No.

ABC-SC0015T
Product Type

Human iPSCs
Cell Type

Induced Pluripotent Stem Cell
Species

Human
Growth Conditions

37 ℃, 5% CO2
Source Organ

Foreskin
Disease

Skin Fibroblasts Of A Cystinosis
Storage

Liquid Nitrogen

HighQC™ Human IPSC From Foreskin Fibroblast provides a cystinosis-specific model for disease mechanism study, cell differentiation, and drug screening.

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  • HighQC™ Human IPSC From Foreskin Fibroblast (Skin Fibroblasts Of A Cystinosis Patient)
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Home | Stem Cells | Induced Pluripotent Stem Cells (iPSCs) | Induced Pluripotent Stem Cells (iPSCs) | HighQC™ Human IPSC From Foreskin Fibroblast (Skin Fibroblasts Of A Cystinosis Patient)

Description

HighQC™ Human iPSC From Foreskin Fibroblasts (Skin Fibroblasts of a Cystinosis Patient) is an induced pluripotent stem cell line derived from primary skin fibroblasts obtained from a patient with cystinosis, a rare autosomal recessive lysosomal storage disorder. The iPSC line was generated using an episomal reprogramming method that includes a proprietary mix of vectors, containing OCT4, SOX2, KLF4, along with p53 antisense, EBNA-1—to enhance reprogramming efficiency while maintaining genomic integrity. They exhibit robust expression of key pluripotency-associated surface markers, such as the glycolipid antigens SSEA-4. The cells undergo rigorous screening and isolation procedures, and are rigorously tested to ensure they are free of contamination from HIV-1, HBV, HCV, syphilis, mycoplasma, fungi, yeast, and bacteria.

Product Code

HighQC™ Human IPSC From Foreskin Fibroblast (Skin Fibroblasts Of A Cystinosis Patient), Human iPSC-Fib-Cystinosis, hIPSC-Fib-Cystinosis, Human Foreskin Fibroblast Derived iPSC Cystinosis
Species

Human
Cat.No

ABC-SC0015T
Product Category

Stem Cells
Size/Quantity

1 vial
Cell Type

Induced Pluripotent Stem Cell
Growth Mode

Adherent
Shipping Info

Dry Ice
Growth Conditions

37 ℃, 5% CO2
Source Organ

Foreskin
Disease

Skin Fibroblasts Of A Cystinosis
Storage

Liquid Nitrogen
Product Type

Human iPSCs

Application

  • HighQC™ Human iPSC From Foreskin Fibroblasts (Skin Fibroblasts of a Cystinosis Patient) serves as a disease-specific in vitro model for investigating the pathogenic mechanisms of lysosomal cystine accumulation associated with CTNS gene mutations. They are particularly valuable for drug screening to identify compounds that correct cystine accumulation, as well as for gene editing studies targeting the defective CTNS gene. They provide a valuable platform for modeling renal, ocular, and systemic complications observed in nephropathic cystinosis.​

Citation

When you publish your research, please cite our product as "AcceGen Biotech Cat.# XXX-0000". In return, we’ll give you a $200 coupon. Simply click here and submit your paper’s PubMed ID (PMID).

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