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HighQC™ Human IPSC From Fibroblast-Kearns-Sayre Syndrome

  • For research use only

Cat No.

ABC-SC2039
Product Type

Human iPSCs
Cell Type

Induced Pluripotent Stem Cell
Species

Human
Growth Conditions

37 ℃, 5% CO2
Source Organ

Fibroblast
Disease

Kearns-Sayre Syndrome
Storage

Liquid Nitrogen

Cell Type: iPSC; Disease: Kearns-Sayre Syndrome; KSS.

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  • HighQC™ Human IPSC From Fibroblast-Kearns-Sayre Syndrome
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Home | Stem Cells | Induced Pluripotent Stem Cells (iPSCs) | Induced Pluripotent Stem Cells (iPSCs) | HighQC™ Human IPSC From Fibroblast-Kearns-Sayre Syndrome

Description

HighQC™ Human IPSCs From Fibroblasts-Kearns-Sayre Syndrome are a disease-affected induced pluripotent stem cell line generated from patient-derived dermal fibroblasts obtained via skin biopsy, carrying Kearns–Sayre syndrome–associated mitochondrial abnormalities, a heritable mitochondrial disorder. These cells exhibit classical human iPSC morphology, including compact colonies with well-defined borders, a high nucleus-to-cytoplasm ratio, and prominent nucleoli. These iPSCs exhibit pluripotency, with the ability to differentiate into all three germ layers under defined conditions, and express the pluripotency marker SSEA-4. The cells undergo rigorous screening and isolation procedures, and are rigorously tested to ensure they are free of contamination from HIV-1, HBV, HCV, Syphilis, Mycoplasma, Fungi, Yeast, and Bacteria.

Product Code

HighQC™ Human IPSC From Fibroblast-Kearns-Sayre Syndrome, HighQC™ hiPSC KSS, hiPSC-KSS, HighQC™ Human Induced Pluripotent Stem Cells From Fibroblast-Kearns-Sayre Syndrome
Species

Human
Cat.No

ABC-SC2039
Product Category

Stem Cells
Size/Quantity

1 vial
Cell Type

Induced Pluripotent Stem Cell
Growth Mode

Adherent
Shipping Info

Dry Ice
Growth Conditions

37 ℃, 5% CO2
Source Organ

Fibroblast
Disease

Kearns-Sayre Syndrome
Storage

Liquid Nitrogen
Product Type

Human iPSCs

Application

  • HighQC™ Human IPSCs From Fibroblasts-Kearns-Sayre Syndrome, also known as Kearns-Sayre Syndrome iPSCs and KSS mitochondrial disease iPSCs, provide a robust in vitro research model for investigating mitochondrial biology and genetic regulation under a patient-relevant background. This cell line can be used to study mitochondrial DNA maintenance, oxidative phosphorylation dynamics, and mitochondrial–nuclear interactions during pluripotency and lineage-specific differentiation. Upon directed differentiation, it supports mechanistic research into how mitochondrial dysfunction influences cellular energy metabolism, differentiation efficiency, and stress responses in developmentally relevant cell types.

Citation

When you publish your research, please cite our product as "AcceGen Biotech Cat.# XXX-0000". In return, we’ll give you a $200 coupon. Simply click here and submit your paper’s PubMed ID (PMID).

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High Viability
To succeed in cell culture
Precision and Reliability
To support a consistent result
Customization Options
Tailed to your research

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