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HighQC™ Human Induced Pluripotent Stem Cells, From Friedreich Ataxia 1

  • For research use only

Cat No.

ABC-SC0230
Product Type

Human iPSCs
Cell Type

Induced Pluripotent Stem Cell
Species

Human
Growth Conditions

37 ℃, 5% CO2
Disease

Friedreich Ataxia 1
Storage

Liquid Nitrogen

Heritable Diseases Disorders of the Nervous System, Trinucleotide Expansions

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  • HighQC™ Human Induced Pluripotent Stem Cells, From Friedreich Ataxia 1
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Home | Stem Cells | Induced Pluripotent Stem Cells (iPSCs) | Induced Pluripotent Stem Cells (iPSCs) | HighQC™ Human Induced Pluripotent Stem Cells, From Friedreich Ataxia 1

Description

HighQC™ Human Induced Pluripotent Stem Cells, From Friedreich Ataxia 1 are derived from patients with Friedreich Ataxia (FRDA). These cells are generated using a retroviral vector to deliver the transcription factors OCT4, SOX2, KLF4, and c-MYC. Donor cells are clinically affected by ataxia, cardiomyopathy, and mild peripheral neuropathy, and are homozygous for the GAA trinucleotide repeat expansion in the FXN gene in the frataxin gene with alleles of approximately 541 and 420 repeats. These cells was evaluated for viability surface antigen expression and alkaline phosphatase activity. Each lot undergoes rigorous screening and isolation procedures, and is rigorously tested to ensure it is free of contamination from HIV-1, HBV, HCV, syphilis, mycoplasma, fungi, yeast, and bacteria.

Product Code

HighQC™ Human Induced Pluripotent Stem Cells, From Friedreich Ataxia 1, Human iPSC-FA1, hIPSC-FA1, Human Induced Pluripotent Stem Cells Friedreich Ataxia
Species

Human
Cat.No

ABC-SC0230
Product Category

Stem Cells
Size/Quantity

1 vial
Cell Type

Induced Pluripotent Stem Cell
Growth Mode

Adherent
Shipping Info

Dry Ice
Growth Conditions

37 ℃, 5% CO2
Disease

Friedreich Ataxia 1
Biosafety Level

1
Storage

Liquid Nitrogen
Product Type

Human iPSCs

Application

  • HighQC™ Human Induced Pluripotent Stem Cells, From Friedreich Ataxia 1 provide a disease-relevant in vitro research platform for investigating the molecular and cellular mechanisms of Friedreich ataxia. These cells retain the characteristic guanine-adenine-adenine trinucleotide repeat expansion in the frataxin gene, enabling genotype-phenotype correlation analyses at the cellular level. They are suitable for studying mitochondrial biology, oxidative stress regulation, iron metabolism dysregulation, and neuronal lineage-specific cellular responses under a human genetic background, serving as valuable stem cells for ataxia research and disease modeling.

Citation

When you publish your research, please cite our product as "AcceGen Biotech Cat.# XXX-0000". In return, we’ll give you a $200 coupon. Simply click here and submit your paper’s PubMed ID (PMID).

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