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HighQC™ Human IPSC From Fibroblast(Mucopolysaccharidosis Type IIIA N-Sulfoglucosamine Sulfohydrolase)

  • For research use only

Cat No.

ABC-SC2033
Product Type

Human iPSCs
Cell Type

Induced Pluripotent Stem Cell
Species

Human
Growth Conditions

37 ℃, 5% CO2
Source Organ

Fibroblast
Disease

Mucopolysaccharidosis Type IIIA N
Storage

Liquid Nitrogen

HighQC™ Human IPSC From Fibroblast (Mucopolysaccharidosis Type IIIA) supports disease modeling, enzyme deficiency research, and SGSH-related iPSC studies.

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  • HighQC™ Human IPSC From Fibroblast(Mucopolysaccharidosis Type IIIA N-Sulfoglucosamine Sulfohydrolase)
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Home | Stem Cells | Induced Pluripotent Stem Cells (iPSCs) | Induced Pluripotent Stem Cells (iPSCs) | HighQC™ Human IPSC From Fibroblast(Mucopolysaccharidosis Type IIIA N-Sulfoglucosamine Sulfohydrolase)

Description

HighQC™ Human iPSCs From Fibroblasts (Mucopolysaccharidosis Type IIIA N-Sulfoglucosamine Sulfohydrolase) are generated from human skin fibroblasts obtained from an individual affected by Mucopolysaccharidosis Type IIIA. This heritable lysosomal storage disorder is caused by deficiency of N-sulfoglucosamine sulfohydrolase (SGSH). These cells display tight colony boundaries, high nuclear-to-cytoplasmic ratios, and clonal growth patterns. Reprogramming was performed using Sendai virus vectors, which transiently express key human transcription factors to initiate the reprogramming process. These iPSCs exhibit pluripotency, with the ability to differentiate into all three germ layers under defined conditions, and express the pluripotency marker SSEA-4. The cells undergo rigorous screening and isolation procedures, and are rigorously tested to ensure they are free of contamination from HIV-1, HBV, HCV, Syphilis, Mycoplasma, Fungi, Yeast, and Bacteria.

Product Code

HighQC™ Human IPSC From Fibroblast (Mucopolysaccharidosis Type IIIA N-Sulfoglucosamine Sulfohydrolase), HighQC™ hiPSC MPS IIIA, hiPSC-MPS3A, HighQC™ Human Induced Pluripotent Stem Cells From Fibroblast-Mucopolysaccharidosis Type IIIA
Species

Human
Cat.No

ABC-SC2033
Product Category

Stem Cells
Size/Quantity

1 vial
Cell Type

Induced Pluripotent Stem Cell
Growth Mode

Adherent
Shipping Info

Dry Ice
Growth Conditions

37 ℃, 5% CO2
Source Organ

Fibroblast
Disease

Mucopolysaccharidosis Type IIIA N
Storage

Liquid Nitrogen
Product Type

Human iPSCs
Gene Info

Gene: SGSH; Mutation: ARG245HIS

Application

  • HighQC™ Human iPSCs From Fibroblasts (Mucopolysaccharidosis Type IIIA N-Sulfoglucosamine Sulfohydrolase), also named MPS IIIA iPSCs, serve as an in vitro model for studying lysosomal function, glycosaminoglycan metabolism, and enzyme deficiency–associated cellular phenotypes. These cells support research into SGSH-related molecular mechanisms, including substrate accumulation, intracellular trafficking, and metabolic pathway dysregulation. In addition, they are well suited for directed differentiation into neural and other relevant lineages, enabling mechanistic investigations of disease-associated cellular dysfunction and gene regulation under controlled experimental conditions.

Citation

When you publish your research, please cite our product as "AcceGen Biotech Cat.# XXX-0000". In return, we’ll give you a $200 coupon. Simply click here and submit your paper’s PubMed ID (PMID).

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